Incontinentia Pigmenti

Authors

F. Iraji Department of Dermatology, Isfahan University of Medical Sciences, Isfahan

G. Faghihi Department of Dermatology, Isfahan University of Medical Sciences, Isfahan

Abstract:

Incontinentia pigmenti (IP) is an uncommon X-linked dominant genodermatosis characterized by four cutaneous stages and frequent association with dental (90%), central nervous system (33%) and ocular (35%) anomalies. The exact pathogenesis of this disorder remains unknown.Herein, we report a newborn girl with inflammatory vesiculobullous and warty skin lesions and a positive family history of IP, with blood leucocytosis (eosinophilia and also lymphocytosis), but no other extracutaneous findings.

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Journal title

Iranian Journal of Medical Sciences

volume 26 issue 3-4

pages 178- 181

publication date 2001-12-01

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